Purpose

The purpose is to assess safety and tolerability of votoplam and to determine whether votoplam slows disease progression in patients with early symptomatic Huntington's disease (HD) compared to the control arm. HTT227 - current compound code (former code is PTC518 from PTC Therapeutics), HTT227 is Novartis code under Novartis sponsorship.

Condition

Eligibility

Eligible Ages
Between 21 Years and 70 Years
Eligible Sex
All
Accepts Healthy Volunteers
No

Inclusion Criteria

  • Signed informed consents must be obtained prior to participation in the study - Ambulatory male or female participants between 21 to 70 years of age, inclusive, on the day of Informed Consent signature - Genetically confirmed HD diagnosis with a cytosine-adenine-guanine (CAG) repeat length of 40 or above. Participants must have prior genetic confirmation and known CAG repeat length obtained prior to screening. - Meets all of the following criteria: - UHDRS IS score ≥90 - UHDRS TFC score = 13 - UHDRS TMS score = 7-25, inclusive - CAP100 ≥ 70 Calculation: CAP = Age at study entry × (CAG length - 30) / 6.49

Exclusion Criteria

  • History of gene therapy or cell transplantation or any other experimental brain surgery for the treatment of HD - Serologic evidence for active viral hepatitis as indicated by: - positive anti-HBc IgM - positive anti-HBc IgG confirmed by positive HBsAg and/or HBV DNA - positive HCV ab test confirmed by positive HCV RNA - Immunodeficiency diseases, including a positive human immunodeficiency virus (HIV) test result - History or current diagnosis of ECG or cardiac abnormalities indicating significant risk of safety for participants such as: - Concomitant clinically significant cardiac arrhythmias, e.g., sustained ventricular tachycardia, and clinically significant second- or third-degree AV block without a pacemaker - History of familial long QT syndrome or known family history of Torsade de Pointes - Women of childbearing potential, defined as all women physiologically capable of becoming pregnant from menarche until becoming post-menopausal, unless they have had surgical bilateral oophorectomy (with or without hysterectomy), total hysterectomy or bilateral salpingectomy at least six weeks before taking study treatment. In the case of oophorectomy alone, the reproductive status of the woman needs to have been confirmed by follow-up hormone level assessment. o WOCBP are excluded unless they are using highly effective methods of contraception (failure rate < 1% per year) while taking study treatment and for 8 months after stopping study treatment. - Pregnant or nursing (breastfeeding) women Other protocol defined inclusion/exclusion criteria may apply

Study Design

Phase
Phase 3
Study Type
Interventional
Allocation
Randomized
Intervention Model
Parallel Assignment
Primary Purpose
Treatment
Masking
Quadruple (Participant, Care Provider, Investigator, Outcomes Assessor)

Arm Groups

ArmDescriptionAssigned Intervention
Experimental
Votoplam
Votoplam (blinded) taken orally, randomized in a 3:2 ratio (Votoplam: Placebo)
  • Drug: Votoplam (blinded)
    Votoplam (blinded) active treatment
    Other names:
    • HTT227
Placebo Comparator
Placebo
Placebo (blinded) taken orally, randomized in a 3:2 ratio (Votoplam: Placebo)
  • Drug: Placebo
    Placebo

Recruiting Locations

Georgetown University
Washington D.C., District of Columbia 20007
Contact:
Robin Kuprewicz
rk1028@georgetown.edu

More Details

Status
Recruiting
Sponsor
Novartis Pharmaceuticals

Study Contact

Novartis Pharmaceuticals
1-888-669-6682
novartis.email@novartis.com

Detailed Description

This study will have a variable double-blind treatment duration of up to 36 months. As part of the study design, not every participant will complete 36 months of treatment. The study consists of 3 periods: - Screening Period: A period of up to 42-days to assess participants eligibility - Double-blind Treatment Period: This period will have variable individual treatment duration, up to 36 months. The double-blind treatment period concludes when ≥50% patients complete Month 36. The maximum treatment duration for an individual participant is 36 months. - Safety Follow-up Period: A period consisting of one safety follow-up visit, conducted on site or by phone call, for all participants not continuing treatment in the separate open-label extension study or discontinuing early. The visit/phone call will take place 30 days after End of Study (EOS)

Notice

Study information shown on this site is derived from ClinicalTrials.gov (a public registry operated by the National Institutes of Health). The listing of studies provided is not certain to be all studies for which you might be eligible. Furthermore, study eligibility requirements can be difficult to understand and may change over time, so it is wise to speak with your medical care provider and individual research study teams when making decisions related to participation.